OncopathologyOncopathologyОнкопатология2618-70193034-3534Publishing House ABV Press70841910.17650/2619-7019-2018-1-1-33-39KAEGLKCase from practiceСлучай из практикиResearch ArticleRecurrent low-grade fibromyxoid sarcoma in the soft tissue of the legРецидивирующая фибромиксоидная саркома низкой степени злокачественности мягких тканей нижней конечностиGorban'N. A.ГорбаньН. А.perovanina@mail.ruKleinaI. V.КлеинаИ. В.
Russian Federation
abv@abvpress.ruPecherskayaM. S.ПечерскаяМ. С.
Russian Federation
abv@abvpress.ruSvyativodaE. A.СвятиводаЕ. А.
Russian Federation
abv@abvpress.ruFedosyukA. M.ФедосюкА. М.
Russian Federation
abv@abvpress.ruIl'inaO. V.ИльинаО. В.
Russian Federation
abv@abvpress.ruN.N. Burdenko Main Military Clinical Hospital, Ministry of Defence of RussiaФГБУ«Главный военный клинический госпиталь им. акад. Н.Н. Бурденко» Минобороны России1802201811333909062026Copyright ©; 2018, ABV-PressCopyright ©; 2018, АБВ-пресс2018ABV-PressАБВ-прессhttps://oncopathology.abvpress.ru/2618-7019/about/editorialPolicieshttps://oncopathology.abvpress.ru/2618-7019/article/view/708419

Low-grade fibromyxoid sarcoma is a relatively rare tumor of deep soft tissue. The difficulties of diagnostics, morphological, immunohisto-chemical and “typical” clinical pictures of this pathology are considered in the article. An algorithm for the differential diagnosis of low-grade fibromyxoid sarcoma and myxoid liposarcoma is given on the example of the clinical case in which the final diagnosis was verified after 40 years from the manifestation of the disease.

Фибромиксоидная саркома низкой степени злокачественности - относительно редкая опухоль глубоких мягких тканей. В статье рассматриваются сложности диагностики, морфологическая, иммуногистохимическая и «типичная» клиническая картина этой патологии. Приводится алгоритм дифференциальной диагностики фибромиксоидной саркомы низкой степени злокачественности и миксоидной липосаркомы на примере клинического случая, в котором окончательный диагноз был верифицирован спустя 40лет от манифестации заболевания.

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